Mohammad Samir Azam Sunny1, Omar Sadeque Khan1,
Md.Mostafizur Rahman2, Md. Aftabuddin3, Asit Baran Adhikary4
Abstract:
Ebstein’s anomaly is a complex malformation involving the tricuspid valve
and the right ventricle. Various surgical techniques, either repair or
replacement of the abnormal tricuspid valve, have been used with variable
results. We report, a case of 32-year –old lady admitted to Bangabandhu
Sheik Mujib Medical University (BSMMU) with fatigability and dyspnea on
exertion for last 2 years. The transthoracic echocardiogram revealed septal
leaflet of tricuspid valve is 18 mm and posterior leaflet is 45 mm displaced
from mitral annulus and tethered to adjacent wall causing severe tricuspid
regurgitation. Per-operatively tricuspid valve anatomy was found diminutive
and beyond repairable. Tricuspid valve replacement was done with 31 mm
Edward Life Science porcine tissue heart valve with placation of atrialized
right ventricle and the patient showed excellent symptomatic improvement.
Ebstein anomaly is a rare and unusual case that was surgically managed
successfully first time in BSMMU.