Congenital Agenesis of Lung – A Case Report

Masum Ahmed1, Md Siddiqur Rahman2, Saiyeedur Rahman3, Abul Hasnat Md Russel4,Khandokar Abul Hasnat Mazmadar5, Sumon Kumar Dhar6, S M Ashraful Alam7

Abstract
The term ‘Agenesis of Lung’ is taken to mean Partial or almost complete absence of growth in the lung.1The rarity of this condition is evident by the infrequent reporting of such cases in literature with prevalence of 34 per million live births. The condition was first discovered accidentally at the autopsy of an adult female in 1673, by De Pozze1. From India, the first case was reported by Muhamed2in
1923, of a left sided pulmonary agenesis in a medicolegal autopsy. Munch Meyer3diagnosed it clinically in 1885. Subsequently a few more case reports have appeared and by 1977, over 200 cases of under development of the lung have been reported.Agenesis of lung,may present in adult life with features of recurrent chest infections and radiologically may mimic many common conditions
presenting as opaque hemithorax with ipsilateral shifting of mediastinum.Here, a case of a young man presenting with frequent attacks of cough expectoration and progressive dyspnoea since childhood,proved to be a case of left pulmonary agenesis on CT scan and bronchoscopy, is to be discussed.

Keywords:Pulmonary agenesis, Recurrent childhood respiratory infection, Herniation of right lung

 

Download PDF