A Case of Idiopathic Hepatic Vena Cava- Budd Chiari Syndrome with Diagnostic Venography

S M Mustafa Zaman1, Md. Mashiul Alam2, Mohammad Atikur Rahman3, Fakhrul Islam Khaled4, Subrata Gain5

 

Abstract
Budd-Chiari Syndrome (BCS) is a potentially life threatening rare hepatic vascular disease that may present as acute or chronic liver failure. It has several varieties depending on etiology and level of obstruction of hepatic blood outflow. In our geographical area BCS presents differently than western countries. Idiopathic hepatic vena cava- Budd Chiari Syndrome (HCV-BCS) is more common in this
area where as prothrombotic conditions are important etiological factors for classical BCS elsewhere. We present a male peasant presenting with subtle symptoms of liver disease and eventually diagnosed as having idiopathic HVCBCS. Invasive venography was used to identify and to detect extent of obstruction.

 

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